The primary mucinous adenocarcinoma of the bladder is an extremely rare urologic entity, which is found in less than 2% of all urinary bladder tumors and is often presented as metastatic. The authors report two cases of bladder adenocarcinoma with epispadias bladder exstrophy complex in two adults. The first case was about a 40-year-old patient referred for management of an EEC evolving since birth. The examination on admission revealed a deterioration in general condition and a bladder plate seat of an ulcero-necrotic tumefaction 3 x 2,5 cm with complete epispadias. The ureteral meatus were visible on each side at the lower part of the plate. Biopsy of the ulcero-necrotic mass revealed a well-differentiated bladder adenocarcinoma. Radical cystectomy and urinary diversion with an ileal conduit, and an expanded local lymphadenectomy was Indicated but the patient died before performing surgery. The second case is about a 28-year-old patient referred for management of an EEC evolving since birth associated with bilateral groin hernia. He had a good general condition, a bladder plate with complete epispadias. Treatment was cystectomy with Bricker urinary. Histo-pathological examination of the specimen reveled mucinous adenocarcinoma of the bladder. After review of the literature, it is a histological type with a poor prognosis and the role of surgery and adjuvant treatment remains to be defined.
Published in | International Journal of Clinical Urology (Volume 8, Issue 1) |
DOI | 10.11648/ijcu.20240801.11 |
Page(s) | 1-3 |
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This is an Open Access article, distributed under the terms of the Creative Commons Attribution 4.0 International License (http://creativecommons.org/licenses/by/4.0/), which permits unrestricted use, distribution and reproduction in any medium or format, provided the original work is properly cited. |
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Exstrophy-Epispadias Complex, Adenocarcinoma, Cystectomy
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APA Style
Sine, B., Feki, M., Bagayogo, N. A., Sarr, A., Ndiath, A., et al. (2024). Adenocarcinoma of the Bladder in Exstrophy-Epispadias Complex in Adult Patients: About Two Cases. International Journal of Clinical Urology, 8(1), 1-3. https://doi.org/10.11648/ijcu.20240801.11
ACS Style
Sine, B.; Feki, M.; Bagayogo, N. A.; Sarr, A.; Ndiath, A., et al. Adenocarcinoma of the Bladder in Exstrophy-Epispadias Complex in Adult Patients: About Two Cases. Int. J. Clin. Urol. 2024, 8(1), 1-3. doi: 10.11648/ijcu.20240801.11
AMA Style
Sine B, Feki M, Bagayogo NA, Sarr A, Ndiath A, et al. Adenocarcinoma of the Bladder in Exstrophy-Epispadias Complex in Adult Patients: About Two Cases. Int J Clin Urol. 2024;8(1):1-3. doi: 10.11648/ijcu.20240801.11
@article{10.11648/ijcu.20240801.11, author = {Babacar Sine and Mouhamed Feki and Ndéye Aissatou Bagayogo and Alioune Sarr and Abdoulaye Ndiath and Amath Thiam and Ndiaga Seck Ndour and Ousmane Sow and El Hadji Malick Diaw and Cyrille Ze Ondo and Yaya Sow and Alain Khassim Ndoye}, title = {Adenocarcinoma of the Bladder in Exstrophy-Epispadias Complex in Adult Patients: About Two Cases}, journal = {International Journal of Clinical Urology}, volume = {8}, number = {1}, pages = {1-3}, doi = {10.11648/ijcu.20240801.11}, url = {https://doi.org/10.11648/ijcu.20240801.11}, eprint = {https://article.sciencepublishinggroup.com/pdf/10.11648.ijcu.20240801.11}, abstract = {The primary mucinous adenocarcinoma of the bladder is an extremely rare urologic entity, which is found in less than 2% of all urinary bladder tumors and is often presented as metastatic. The authors report two cases of bladder adenocarcinoma with epispadias bladder exstrophy complex in two adults. The first case was about a 40-year-old patient referred for management of an EEC evolving since birth. The examination on admission revealed a deterioration in general condition and a bladder plate seat of an ulcero-necrotic tumefaction 3 x 2,5 cm with complete epispadias. The ureteral meatus were visible on each side at the lower part of the plate. Biopsy of the ulcero-necrotic mass revealed a well-differentiated bladder adenocarcinoma. Radical cystectomy and urinary diversion with an ileal conduit, and an expanded local lymphadenectomy was Indicated but the patient died before performing surgery. The second case is about a 28-year-old patient referred for management of an EEC evolving since birth associated with bilateral groin hernia. He had a good general condition, a bladder plate with complete epispadias. Treatment was cystectomy with Bricker urinary. Histo-pathological examination of the specimen reveled mucinous adenocarcinoma of the bladder. After review of the literature, it is a histological type with a poor prognosis and the role of surgery and adjuvant treatment remains to be defined. }, year = {2024} }
TY - JOUR T1 - Adenocarcinoma of the Bladder in Exstrophy-Epispadias Complex in Adult Patients: About Two Cases AU - Babacar Sine AU - Mouhamed Feki AU - Ndéye Aissatou Bagayogo AU - Alioune Sarr AU - Abdoulaye Ndiath AU - Amath Thiam AU - Ndiaga Seck Ndour AU - Ousmane Sow AU - El Hadji Malick Diaw AU - Cyrille Ze Ondo AU - Yaya Sow AU - Alain Khassim Ndoye Y1 - 2024/02/01 PY - 2024 N1 - https://doi.org/10.11648/ijcu.20240801.11 DO - 10.11648/ijcu.20240801.11 T2 - International Journal of Clinical Urology JF - International Journal of Clinical Urology JO - International Journal of Clinical Urology SP - 1 EP - 3 PB - Science Publishing Group SN - 2640-1355 UR - https://doi.org/10.11648/ijcu.20240801.11 AB - The primary mucinous adenocarcinoma of the bladder is an extremely rare urologic entity, which is found in less than 2% of all urinary bladder tumors and is often presented as metastatic. The authors report two cases of bladder adenocarcinoma with epispadias bladder exstrophy complex in two adults. The first case was about a 40-year-old patient referred for management of an EEC evolving since birth. The examination on admission revealed a deterioration in general condition and a bladder plate seat of an ulcero-necrotic tumefaction 3 x 2,5 cm with complete epispadias. The ureteral meatus were visible on each side at the lower part of the plate. Biopsy of the ulcero-necrotic mass revealed a well-differentiated bladder adenocarcinoma. Radical cystectomy and urinary diversion with an ileal conduit, and an expanded local lymphadenectomy was Indicated but the patient died before performing surgery. The second case is about a 28-year-old patient referred for management of an EEC evolving since birth associated with bilateral groin hernia. He had a good general condition, a bladder plate with complete epispadias. Treatment was cystectomy with Bricker urinary. Histo-pathological examination of the specimen reveled mucinous adenocarcinoma of the bladder. After review of the literature, it is a histological type with a poor prognosis and the role of surgery and adjuvant treatment remains to be defined. VL - 8 IS - 1 ER -