A Successful Correction of a Truncus Arteriosus in an 8-Year-Old Girl with Functional Pulmonary Stenosis by a Particular Opening of the Truncal Valve

Karima Hami; Rida Ajaja; Younes Cheikhaoui

doi:doi:10.11648/j.ijcts.20220806.11

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A Successful Correction of a Truncus Arteriosus in an 8-Year-Old Girl with Functional Pulmonary Stenosis by a Particular Opening of the Truncal Valve

Karima Hami, Rida Ajaja, Younes Cheikhaoui

Published in International Journal of Cardiovascular and Thoracic Surgery (Volume 8, Issue 6)

Received: 25 December 2022 Accepted: 27 January 2023 Published: 9 February 2023

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Abstract

Background: Truncus arteriosus is a rare congenital heart malformation requiring repair in the neonatal period. Without correction, the majority of patients die within the first year of life. However, this case shows that some patients remain operable even at an advanced age. Case presentation: We report the case of an 8-year-old girl with type 2 truncus arteriosus with pulmonary vascular protection by a particular opening of the truncal valve partially obstructing the origin of the pulmonary artery in systole and causing a reduction in pulmonary flow. The initial evaluation based on the clinical presentation, the electrocardiogram and the echocardiography showed a significant elevation of the pressures of the right ventricle with a functional stenosis at the origin of the pulmonary artery. Hemodynamic exploration demonstrated that the pulmonary arterial hypertension is reversible, thereby the patient was successfully operated. Conclusion: The objective of this observation is to demonstrate that truncus arteriosus referred late does not eliminate the possibility of complete surgical repair, which underlines the importance of an exhaustive evaluation of these patients based on several arguments.

Published in	International Journal of Cardiovascular and Thoracic Surgery (Volume 8, Issue 6)
DOI	10.11648/j.ijcts.20220806.11
Page(s)	59-62
Creative Commons	This is an Open Access article, distributed under the terms of the Creative Commons Attribution 4.0 International License (http://creativecommons.org/licenses/by/4.0/), which permits unrestricted use, distribution and reproduction in any medium or format, provided the original work is properly cited.
Copyright	Copyright © The Author(s), 2024. Published by Science Publishing Group

Keywords

Congenital Heart Defect, Truncus Arteriosus, Pulmonary Hypertension

References

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APA Style

Karima Hami, Rida Ajaja, Younes Cheikhaoui. (2023). A Successful Correction of a Truncus Arteriosus in an 8-Year-Old Girl with Functional Pulmonary Stenosis by a Particular Opening of the Truncal Valve. International Journal of Cardiovascular and Thoracic Surgery, 8(6), 59-62. https://doi.org/10.11648/j.ijcts.20220806.11

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ACS Style

Karima Hami; Rida Ajaja; Younes Cheikhaoui. A Successful Correction of a Truncus Arteriosus in an 8-Year-Old Girl with Functional Pulmonary Stenosis by a Particular Opening of the Truncal Valve. Int. J. Cardiovasc. Thorac. Surg. 2023, 8(6), 59-62. doi: 10.11648/j.ijcts.20220806.11

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AMA Style

Karima Hami, Rida Ajaja, Younes Cheikhaoui. A Successful Correction of a Truncus Arteriosus in an 8-Year-Old Girl with Functional Pulmonary Stenosis by a Particular Opening of the Truncal Valve. Int J Cardiovasc Thorac Surg. 2023;8(6):59-62. doi: 10.11648/j.ijcts.20220806.11

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@article{10.11648/j.ijcts.20220806.11,
  author = {Karima Hami and Rida Ajaja and Younes Cheikhaoui},
  title = {A Successful Correction of a Truncus Arteriosus in an 8-Year-Old Girl with Functional Pulmonary Stenosis by a Particular Opening of the Truncal Valve},
  journal = {International Journal of Cardiovascular and Thoracic Surgery},
  volume = {8},
  number = {6},
  pages = {59-62},
  doi = {10.11648/j.ijcts.20220806.11},
  url = {https://doi.org/10.11648/j.ijcts.20220806.11},
  eprint = {https://article.sciencepublishinggroup.com/pdf/10.11648.j.ijcts.20220806.11},
  abstract = {Background: Truncus arteriosus is a rare congenital heart malformation requiring repair in the neonatal period. Without correction, the majority of patients die within the first year of life. However, this case shows that some patients remain operable even at an advanced age. Case presentation: We report the case of an 8-year-old girl with type 2 truncus arteriosus with pulmonary vascular protection by a particular opening of the truncal valve partially obstructing the origin of the pulmonary artery in systole and causing a reduction in pulmonary flow. The initial evaluation based on the clinical presentation, the electrocardiogram and the echocardiography showed a significant elevation of the pressures of the right ventricle with a functional stenosis at the origin of the pulmonary artery. Hemodynamic exploration demonstrated that the pulmonary arterial hypertension is reversible, thereby the patient was successfully operated. Conclusion: The objective of this observation is to demonstrate that truncus arteriosus referred late does not eliminate the possibility of complete surgical repair, which underlines the importance of an exhaustive evaluation of these patients based on several arguments.},
 year = {2023}
}

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TY  - JOUR
T1  - A Successful Correction of a Truncus Arteriosus in an 8-Year-Old Girl with Functional Pulmonary Stenosis by a Particular Opening of the Truncal Valve
AU  - Karima Hami
AU  - Rida Ajaja
AU  - Younes Cheikhaoui
Y1  - 2023/02/09
PY  - 2023
N1  - https://doi.org/10.11648/j.ijcts.20220806.11
DO  - 10.11648/j.ijcts.20220806.11
T2  - International Journal of Cardiovascular and Thoracic Surgery
JF  - International Journal of Cardiovascular and Thoracic Surgery
JO  - International Journal of Cardiovascular and Thoracic Surgery
SP  - 59
EP  - 62
PB  - Science Publishing Group
SN  - 2575-4882
UR  - https://doi.org/10.11648/j.ijcts.20220806.11
AB  - Background: Truncus arteriosus is a rare congenital heart malformation requiring repair in the neonatal period. Without correction, the majority of patients die within the first year of life. However, this case shows that some patients remain operable even at an advanced age. Case presentation: We report the case of an 8-year-old girl with type 2 truncus arteriosus with pulmonary vascular protection by a particular opening of the truncal valve partially obstructing the origin of the pulmonary artery in systole and causing a reduction in pulmonary flow. The initial evaluation based on the clinical presentation, the electrocardiogram and the echocardiography showed a significant elevation of the pressures of the right ventricle with a functional stenosis at the origin of the pulmonary artery. Hemodynamic exploration demonstrated that the pulmonary arterial hypertension is reversible, thereby the patient was successfully operated. Conclusion: The objective of this observation is to demonstrate that truncus arteriosus referred late does not eliminate the possibility of complete surgical repair, which underlines the importance of an exhaustive evaluation of these patients based on several arguments.
VL  - 8
IS  - 6
ER  -

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Author Information

Karima Hami

Congenital Cardiology Unit, Cheikh Zaid Hospital, Abulcassis University, Rabat, Morocco
Rida Ajaja

Congenital Cardiology Unit, Cheikh Zaid Hospital, Abulcassis University, Rabat, Morocco
Younes Cheikhaoui

Congenital Cardiology Unit, Cheikh Zaid Hospital, Abulcassis University, Rabat, Morocco

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Plain Text BibTeX RIS

APA Style

Karima Hami, Rida Ajaja, Younes Cheikhaoui. (2023). A Successful Correction of a Truncus Arteriosus in an 8-Year-Old Girl with Functional Pulmonary Stenosis by a Particular Opening of the Truncal Valve. International Journal of Cardiovascular and Thoracic Surgery, 8(6), 59-62. https://doi.org/10.11648/j.ijcts.20220806.11

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ACS Style

Karima Hami; Rida Ajaja; Younes Cheikhaoui. A Successful Correction of a Truncus Arteriosus in an 8-Year-Old Girl with Functional Pulmonary Stenosis by a Particular Opening of the Truncal Valve. Int. J. Cardiovasc. Thorac. Surg. 2023, 8(6), 59-62. doi: 10.11648/j.ijcts.20220806.11

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AMA Style

Karima Hami, Rida Ajaja, Younes Cheikhaoui. A Successful Correction of a Truncus Arteriosus in an 8-Year-Old Girl with Functional Pulmonary Stenosis by a Particular Opening of the Truncal Valve. Int J Cardiovasc Thorac Surg. 2023;8(6):59-62. doi: 10.11648/j.ijcts.20220806.11

Copy | Download

@article{10.11648/j.ijcts.20220806.11,
  author = {Karima Hami and Rida Ajaja and Younes Cheikhaoui},
  title = {A Successful Correction of a Truncus Arteriosus in an 8-Year-Old Girl with Functional Pulmonary Stenosis by a Particular Opening of the Truncal Valve},
  journal = {International Journal of Cardiovascular and Thoracic Surgery},
  volume = {8},
  number = {6},
  pages = {59-62},
  doi = {10.11648/j.ijcts.20220806.11},
  url = {https://doi.org/10.11648/j.ijcts.20220806.11},
  eprint = {https://article.sciencepublishinggroup.com/pdf/10.11648.j.ijcts.20220806.11},
  abstract = {Background: Truncus arteriosus is a rare congenital heart malformation requiring repair in the neonatal period. Without correction, the majority of patients die within the first year of life. However, this case shows that some patients remain operable even at an advanced age. Case presentation: We report the case of an 8-year-old girl with type 2 truncus arteriosus with pulmonary vascular protection by a particular opening of the truncal valve partially obstructing the origin of the pulmonary artery in systole and causing a reduction in pulmonary flow. The initial evaluation based on the clinical presentation, the electrocardiogram and the echocardiography showed a significant elevation of the pressures of the right ventricle with a functional stenosis at the origin of the pulmonary artery. Hemodynamic exploration demonstrated that the pulmonary arterial hypertension is reversible, thereby the patient was successfully operated. Conclusion: The objective of this observation is to demonstrate that truncus arteriosus referred late does not eliminate the possibility of complete surgical repair, which underlines the importance of an exhaustive evaluation of these patients based on several arguments.},
 year = {2023}
}

Copy | Download

TY  - JOUR
T1  - A Successful Correction of a Truncus Arteriosus in an 8-Year-Old Girl with Functional Pulmonary Stenosis by a Particular Opening of the Truncal Valve
AU  - Karima Hami
AU  - Rida Ajaja
AU  - Younes Cheikhaoui
Y1  - 2023/02/09
PY  - 2023
N1  - https://doi.org/10.11648/j.ijcts.20220806.11
DO  - 10.11648/j.ijcts.20220806.11
T2  - International Journal of Cardiovascular and Thoracic Surgery
JF  - International Journal of Cardiovascular and Thoracic Surgery
JO  - International Journal of Cardiovascular and Thoracic Surgery
SP  - 59
EP  - 62
PB  - Science Publishing Group
SN  - 2575-4882
UR  - https://doi.org/10.11648/j.ijcts.20220806.11
AB  - Background: Truncus arteriosus is a rare congenital heart malformation requiring repair in the neonatal period. Without correction, the majority of patients die within the first year of life. However, this case shows that some patients remain operable even at an advanced age. Case presentation: We report the case of an 8-year-old girl with type 2 truncus arteriosus with pulmonary vascular protection by a particular opening of the truncal valve partially obstructing the origin of the pulmonary artery in systole and causing a reduction in pulmonary flow. The initial evaluation based on the clinical presentation, the electrocardiogram and the echocardiography showed a significant elevation of the pressures of the right ventricle with a functional stenosis at the origin of the pulmonary artery. Hemodynamic exploration demonstrated that the pulmonary arterial hypertension is reversible, thereby the patient was successfully operated. Conclusion: The objective of this observation is to demonstrate that truncus arteriosus referred late does not eliminate the possibility of complete surgical repair, which underlines the importance of an exhaustive evaluation of these patients based on several arguments.
VL  - 8
IS  - 6
ER  -

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