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Imaging Diagnosis of Situs Inversus, Persistence of the Left Superior Vena Cava, Renal Agenesis and Anomaly of the Retroperitoneal Vessels in Niamey: A Case Report

Received: 17 December 2023    Accepted: 2 January 2024    Published: 18 January 2024
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Abstract

Introduction: Situs inversus is a rare congenital malformation. It can be associated with other malformations. It is often discovered incidentally by medical imaging. The latter also makes it possible to take stock of all associated malformations. Observation: The authors report a particular association in a 4-year-old male patient. Following a transthoracic cardiac Doppler ultrasound indicated for dyspnea at the slightest effort. The examination revealed dextrocardia, minimal membranous septum interventricular communication with left-right shunt, ostium primum inter-atrial communication measured at 6 mm with moderate impact on the left atrium, good systolic function of both ventricles, thin heart valves, dry pericardium. The chest x-ray requested systematically highlighted dextrocardia, enlargement of the upper mediastinum, and a gastric air pocket visible under the right diaphragmatic dome. The thoraco-abdomino-pelvic scan carried out made it possible to demonstrate that the situs inversus was complete and associated with other anomalies. It was a type 3b superior cava venous return anomaly with a single left kidney and an anomaly of the retroperitoneal vessels. Conclusion: Situs inversus is a rare and particular congenital anomaly because it can be associated with several types of malformations, sometimes very complex. Hence the interest in carrying out a complete imaging assessment in cases of situs inversus.

Published in International Journal of Medical Imaging (Volume 12, Issue 1)
DOI 10.11648/j.ijmi.20241201.11
Page(s) 1-4
Creative Commons

This is an Open Access article, distributed under the terms of the Creative Commons Attribution 4.0 International License (http://creativecommons.org/licenses/by/4.0/), which permits unrestricted use, distribution and reproduction in any medium or format, provided the original work is properly cited.

Copyright

Copyright © The Author(s), 2024. Published by Science Publishing Group

Keywords

Situs Inversus, Congenital Heart Disease, PVCSG, Renal Agenesis, Retroperitoneal Vessel Anomaly, Left IVC, Niamey

References
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Cite This Article
  • APA Style

    Inoussa, B. D., Tijani, M. H., Habiba, T. M. S., Rabiou, S. M., Matallah, S., et al. (2024). Imaging Diagnosis of Situs Inversus, Persistence of the Left Superior Vena Cava, Renal Agenesis and Anomaly of the Retroperitoneal Vessels in Niamey: A Case Report. International Journal of Medical Imaging, 12(1), 1-4. https://doi.org/10.11648/j.ijmi.20241201.11

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    ACS Style

    Inoussa, B. D.; Tijani, M. H.; Habiba, T. M. S.; Rabiou, S. M.; Matallah, S., et al. Imaging Diagnosis of Situs Inversus, Persistence of the Left Superior Vena Cava, Renal Agenesis and Anomaly of the Retroperitoneal Vessels in Niamey: A Case Report. Int. J. Med. Imaging 2024, 12(1), 1-4. doi: 10.11648/j.ijmi.20241201.11

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    AMA Style

    Inoussa BD, Tijani MH, Habiba TMS, Rabiou SM, Matallah S, et al. Imaging Diagnosis of Situs Inversus, Persistence of the Left Superior Vena Cava, Renal Agenesis and Anomaly of the Retroperitoneal Vessels in Niamey: A Case Report. Int J Med Imaging. 2024;12(1):1-4. doi: 10.11648/j.ijmi.20241201.11

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  • @article{10.11648/j.ijmi.20241201.11,
      author = {Bako Daouda Inoussa and Mahamat Hissene Tijani and Tinao Mahamane Sani Habiba and Sani Mamane Rabiou and Sako Matallah and Akpovi Alexandre},
      title = {Imaging Diagnosis of Situs Inversus, Persistence of the Left Superior Vena Cava, Renal Agenesis and Anomaly of the Retroperitoneal Vessels in Niamey: A Case Report},
      journal = {International Journal of Medical Imaging},
      volume = {12},
      number = {1},
      pages = {1-4},
      doi = {10.11648/j.ijmi.20241201.11},
      url = {https://doi.org/10.11648/j.ijmi.20241201.11},
      eprint = {https://article.sciencepublishinggroup.com/pdf/10.11648.j.ijmi.20241201.11},
      abstract = {Introduction: Situs inversus is a rare congenital malformation. It can be associated with other malformations. It is often discovered incidentally by medical imaging. The latter also makes it possible to take stock of all associated malformations. Observation: The authors report a particular association in a 4-year-old male patient. Following a transthoracic cardiac Doppler ultrasound indicated for dyspnea at the slightest effort. The examination revealed dextrocardia, minimal membranous septum interventricular communication with left-right shunt, ostium primum inter-atrial communication measured at 6 mm with moderate impact on the left atrium, good systolic function of both ventricles, thin heart valves, dry pericardium. The chest x-ray requested systematically highlighted dextrocardia, enlargement of the upper mediastinum, and a gastric air pocket visible under the right diaphragmatic dome. The thoraco-abdomino-pelvic scan carried out made it possible to demonstrate that the situs inversus was complete and associated with other anomalies. It was a type 3b superior cava venous return anomaly with a single left kidney and an anomaly of the retroperitoneal vessels. Conclusion: Situs inversus is a rare and particular congenital anomaly because it can be associated with several types of malformations, sometimes very complex. Hence the interest in carrying out a complete imaging assessment in cases of situs inversus.
    },
     year = {2024}
    }
    

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    T1  - Imaging Diagnosis of Situs Inversus, Persistence of the Left Superior Vena Cava, Renal Agenesis and Anomaly of the Retroperitoneal Vessels in Niamey: A Case Report
    AU  - Bako Daouda Inoussa
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    AU  - Tinao Mahamane Sani Habiba
    AU  - Sani Mamane Rabiou
    AU  - Sako Matallah
    AU  - Akpovi Alexandre
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    JF  - International Journal of Medical Imaging
    JO  - International Journal of Medical Imaging
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    EP  - 4
    PB  - Science Publishing Group
    SN  - 2330-832X
    UR  - https://doi.org/10.11648/j.ijmi.20241201.11
    AB  - Introduction: Situs inversus is a rare congenital malformation. It can be associated with other malformations. It is often discovered incidentally by medical imaging. The latter also makes it possible to take stock of all associated malformations. Observation: The authors report a particular association in a 4-year-old male patient. Following a transthoracic cardiac Doppler ultrasound indicated for dyspnea at the slightest effort. The examination revealed dextrocardia, minimal membranous septum interventricular communication with left-right shunt, ostium primum inter-atrial communication measured at 6 mm with moderate impact on the left atrium, good systolic function of both ventricles, thin heart valves, dry pericardium. The chest x-ray requested systematically highlighted dextrocardia, enlargement of the upper mediastinum, and a gastric air pocket visible under the right diaphragmatic dome. The thoraco-abdomino-pelvic scan carried out made it possible to demonstrate that the situs inversus was complete and associated with other anomalies. It was a type 3b superior cava venous return anomaly with a single left kidney and an anomaly of the retroperitoneal vessels. Conclusion: Situs inversus is a rare and particular congenital anomaly because it can be associated with several types of malformations, sometimes very complex. Hence the interest in carrying out a complete imaging assessment in cases of situs inversus.
    
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Author Information
  • Radiology and Medical Imaging Department, General Reference Hospital, Niamey, Niger; Faculty of Health Sciences, Abdou Moumouni University, Niamey, Niger

  • Radiology and Medical Imaging Department, General Reference Hospital, Niamey, Niger

  • Radiology and Medical Imaging Department, General Reference Hospital, Niamey, Niger

  • Faculty of Health Sciences, Abdou Moumouni University, Niamey, Niger; Thoracic and Vascular Surgery Department, Reference General Hospital, Niamey, Niger

  • Radiology and Medical Imaging Department, General Reference Hospital, Niamey, Niger

  • Radiology and Medical Imaging Department, General Reference Hospital, Niamey, Niger

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