Choledocal cyst (CC) is a rare congenital cystic dilation of bile duct and can be associated with serious complications including malignancy and inflammation of the surrounding anatomy. Approximately 80% of CC is diagnosed in infants and young children in their first decade of life. Complete surgical resection is recommended in patients with choledochal malformations with excellent outcome. Hereby we aimed to describe diagnosis and management aspects of choledochal cyst. A two years old girl complained intermittent abdominal pain in her upper right quadrant abdomen, accompanied with fever, nausea and vomiting and decrease of appetite. Physical examination, we found jaundice on sclera and palpabled liver 2 fingers below the costal arch. Abdominal ultrasound revealed cystic mass in right lower lobe, suggestive of hepatic cyst with inflammation of cystic head of pancreas and minimal free fluid in lumen. Abdominal CT-scan without contrast showed a choledocal cyst classified as Todani Type IV. A cyst in the bile duct was found during surgical procedure. In conclusion choledocal cyst as one of the differential diagnoses in children, which is characterized by intermittent right upper abdominal pain, jaundice and fever. Appropriate surgical measures should be undertaken to avoid complications.
| Published in | American Journal of Pediatrics (Volume 8, Issue 3) |
| DOI | 10.11648/j.ajp.20220803.13 |
| Page(s) | 168-172 |
| Creative Commons |
This is an Open Access article, distributed under the terms of the Creative Commons Attribution 4.0 International License (http://creativecommons.org/licenses/by/4.0/), which permits unrestricted use, distribution and reproduction in any medium or format, provided the original work is properly cited. |
| Copyright |
Copyright © The Author(s), 2022. Published by Science Publishing Group |
Children, Choledocal Cysts, Extrahepatal Cholestasis
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APA Style
Luh Made Diah Wulandari Artana, I Gusti Ngurah Sanjaya Putra, Kadek Deddy Ariyanta, I Putu Gede Karyana, Ni Nyoman Metriani Nesa, et al. (2022). Extrahepatal Cholestasis Due to Choledochal Cyst Type Iv Todani Classification in Two Years Old Girl. American Journal of Pediatrics, 8(3), 168-172. https://doi.org/10.11648/j.ajp.20220803.13
ACS Style
Luh Made Diah Wulandari Artana; I Gusti Ngurah Sanjaya Putra; Kadek Deddy Ariyanta; I Putu Gede Karyana; Ni Nyoman Metriani Nesa, et al. Extrahepatal Cholestasis Due to Choledochal Cyst Type Iv Todani Classification in Two Years Old Girl. Am. J. Pediatr. 2022, 8(3), 168-172. doi: 10.11648/j.ajp.20220803.13
AMA Style
Luh Made Diah Wulandari Artana, I Gusti Ngurah Sanjaya Putra, Kadek Deddy Ariyanta, I Putu Gede Karyana, Ni Nyoman Metriani Nesa, et al. Extrahepatal Cholestasis Due to Choledochal Cyst Type Iv Todani Classification in Two Years Old Girl. Am J Pediatr. 2022;8(3):168-172. doi: 10.11648/j.ajp.20220803.13
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author = {Luh Made Diah Wulandari Artana and I Gusti Ngurah Sanjaya Putra and Kadek Deddy Ariyanta and I Putu Gede Karyana and Ni Nyoman Metriani Nesa and I Made Darmajaya},
title = {Extrahepatal Cholestasis Due to Choledochal Cyst Type Iv Todani Classification in Two Years Old Girl},
journal = {American Journal of Pediatrics},
volume = {8},
number = {3},
pages = {168-172},
doi = {10.11648/j.ajp.20220803.13},
url = {https://doi.org/10.11648/j.ajp.20220803.13},
eprint = {https://article.sciencepublishinggroup.com/pdf/10.11648.j.ajp.20220803.13},
abstract = {Choledocal cyst (CC) is a rare congenital cystic dilation of bile duct and can be associated with serious complications including malignancy and inflammation of the surrounding anatomy. Approximately 80% of CC is diagnosed in infants and young children in their first decade of life. Complete surgical resection is recommended in patients with choledochal malformations with excellent outcome. Hereby we aimed to describe diagnosis and management aspects of choledochal cyst. A two years old girl complained intermittent abdominal pain in her upper right quadrant abdomen, accompanied with fever, nausea and vomiting and decrease of appetite. Physical examination, we found jaundice on sclera and palpabled liver 2 fingers below the costal arch. Abdominal ultrasound revealed cystic mass in right lower lobe, suggestive of hepatic cyst with inflammation of cystic head of pancreas and minimal free fluid in lumen. Abdominal CT-scan without contrast showed a choledocal cyst classified as Todani Type IV. A cyst in the bile duct was found during surgical procedure. In conclusion choledocal cyst as one of the differential diagnoses in children, which is characterized by intermittent right upper abdominal pain, jaundice and fever. Appropriate surgical measures should be undertaken to avoid complications.},
year = {2022}
}
TY - JOUR T1 - Extrahepatal Cholestasis Due to Choledochal Cyst Type Iv Todani Classification in Two Years Old Girl AU - Luh Made Diah Wulandari Artana AU - I Gusti Ngurah Sanjaya Putra AU - Kadek Deddy Ariyanta AU - I Putu Gede Karyana AU - Ni Nyoman Metriani Nesa AU - I Made Darmajaya Y1 - 2022/07/28 PY - 2022 N1 - https://doi.org/10.11648/j.ajp.20220803.13 DO - 10.11648/j.ajp.20220803.13 T2 - American Journal of Pediatrics JF - American Journal of Pediatrics JO - American Journal of Pediatrics SP - 168 EP - 172 PB - Science Publishing Group SN - 2472-0909 UR - https://doi.org/10.11648/j.ajp.20220803.13 AB - Choledocal cyst (CC) is a rare congenital cystic dilation of bile duct and can be associated with serious complications including malignancy and inflammation of the surrounding anatomy. Approximately 80% of CC is diagnosed in infants and young children in their first decade of life. Complete surgical resection is recommended in patients with choledochal malformations with excellent outcome. Hereby we aimed to describe diagnosis and management aspects of choledochal cyst. A two years old girl complained intermittent abdominal pain in her upper right quadrant abdomen, accompanied with fever, nausea and vomiting and decrease of appetite. Physical examination, we found jaundice on sclera and palpabled liver 2 fingers below the costal arch. Abdominal ultrasound revealed cystic mass in right lower lobe, suggestive of hepatic cyst with inflammation of cystic head of pancreas and minimal free fluid in lumen. Abdominal CT-scan without contrast showed a choledocal cyst classified as Todani Type IV. A cyst in the bile duct was found during surgical procedure. In conclusion choledocal cyst as one of the differential diagnoses in children, which is characterized by intermittent right upper abdominal pain, jaundice and fever. Appropriate surgical measures should be undertaken to avoid complications. VL - 8 IS - 3 ER -
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