Background: Congenital mesoblastic nephroma (CMN) is a rare mesenchymal renal tumor of the newborn. The objective of this study was to review the clinical particularities, paraclinical and therapeutic characteristics of this tumor. It is about a case report of pediatric patient admitted to a Pediatric Neonatal Reanimation, A. Harouchi Hospital, Ibn Rochd university Hospital centre, Casablanca. Results: We report the observation of a 4-day premature newborn who was hospitalized for exploration of an abdominal mass occupying the right flank since birth. Abdominal ultrasonography revealed a predominantly fleshy right solidocystic renal mass, a site of calcifications laminating the cortex, measuring 57x33x58, with minimal pyelocaliceal dilatation and diffuse infiltration of perrenal fat. The CT scan revealed a kidney increased in size, seat of a voluminous mass rather well limited, of tissue density, heterogeneous, seat of necrosis, realizing a sign of the spur, measuring 40x47x58mm. The diagnosis was confirmed by a kidney biopsy. Conclusion: Mesoblastic nephroma is considered a benign tumor. The diagnosis is discussed on the basis of clinical data, ultrasound and CT scan. Surgery is the primary treatment for NMC and is based on extended nephrectomy. Most patients with NMC have a favorable outcome, the overall prognosis is very good.
| Published in | American Journal of Pediatrics (Volume 9, Issue 1) |
| DOI | 10.11648/j.ajp.20230901.17 |
| Page(s) | 55-58 |
| Creative Commons |
This is an Open Access article, distributed under the terms of the Creative Commons Attribution 4.0 International License (http://creativecommons.org/licenses/by/4.0/), which permits unrestricted use, distribution and reproduction in any medium or format, provided the original work is properly cited. |
| Copyright |
Copyright © The Author(s), 2023. Published by Science Publishing Group |
Renal Tumor, Congenital Mesoblastic Nephroma, Neonatology
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APA Style
Karima Ryouni, Imane Ain El Hayat, Mouna Lehlimi, Amal Badre, Mounir Chemsi, et al. (2023). Congenital Mesoblastic Nephroma in a Newborn: Case Report. American Journal of Pediatrics, 9(1), 55-58. https://doi.org/10.11648/j.ajp.20230901.17
ACS Style
Karima Ryouni; Imane Ain El Hayat; Mouna Lehlimi; Amal Badre; Mounir Chemsi, et al. Congenital Mesoblastic Nephroma in a Newborn: Case Report. Am. J. Pediatr. 2023, 9(1), 55-58. doi: 10.11648/j.ajp.20230901.17
AMA Style
Karima Ryouni, Imane Ain El Hayat, Mouna Lehlimi, Amal Badre, Mounir Chemsi, et al. Congenital Mesoblastic Nephroma in a Newborn: Case Report. Am J Pediatr. 2023;9(1):55-58. doi: 10.11648/j.ajp.20230901.17
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Download@article{10.11648/j.ajp.20230901.17,
author = {Karima Ryouni and Imane Ain El Hayat and Mouna Lehlimi and Amal Badre and Mounir Chemsi and Abdelhak Habzi and Said Benomar and Asmae El Kebir and Nisrine Bennani},
title = {Congenital Mesoblastic Nephroma in a Newborn: Case Report},
journal = {American Journal of Pediatrics},
volume = {9},
number = {1},
pages = {55-58},
doi = {10.11648/j.ajp.20230901.17},
url = {https://doi.org/10.11648/j.ajp.20230901.17},
eprint = {https://article.sciencepublishinggroup.com/pdf/10.11648.j.ajp.20230901.17},
abstract = {Background: Congenital mesoblastic nephroma (CMN) is a rare mesenchymal renal tumor of the newborn. The objective of this study was to review the clinical particularities, paraclinical and therapeutic characteristics of this tumor. It is about a case report of pediatric patient admitted to a Pediatric Neonatal Reanimation, A. Harouchi Hospital, Ibn Rochd university Hospital centre, Casablanca. Results: We report the observation of a 4-day premature newborn who was hospitalized for exploration of an abdominal mass occupying the right flank since birth. Abdominal ultrasonography revealed a predominantly fleshy right solidocystic renal mass, a site of calcifications laminating the cortex, measuring 57x33x58, with minimal pyelocaliceal dilatation and diffuse infiltration of perrenal fat. The CT scan revealed a kidney increased in size, seat of a voluminous mass rather well limited, of tissue density, heterogeneous, seat of necrosis, realizing a sign of the spur, measuring 40x47x58mm. The diagnosis was confirmed by a kidney biopsy. Conclusion: Mesoblastic nephroma is considered a benign tumor. The diagnosis is discussed on the basis of clinical data, ultrasound and CT scan. Surgery is the primary treatment for NMC and is based on extended nephrectomy. Most patients with NMC have a favorable outcome, the overall prognosis is very good.},
year = {2023}
}
TY - JOUR T1 - Congenital Mesoblastic Nephroma in a Newborn: Case Report AU - Karima Ryouni AU - Imane Ain El Hayat AU - Mouna Lehlimi AU - Amal Badre AU - Mounir Chemsi AU - Abdelhak Habzi AU - Said Benomar AU - Asmae El Kebir AU - Nisrine Bennani Y1 - 2023/03/31 PY - 2023 N1 - https://doi.org/10.11648/j.ajp.20230901.17 DO - 10.11648/j.ajp.20230901.17 T2 - American Journal of Pediatrics JF - American Journal of Pediatrics JO - American Journal of Pediatrics SP - 55 EP - 58 PB - Science Publishing Group SN - 2472-0909 UR - https://doi.org/10.11648/j.ajp.20230901.17 AB - Background: Congenital mesoblastic nephroma (CMN) is a rare mesenchymal renal tumor of the newborn. The objective of this study was to review the clinical particularities, paraclinical and therapeutic characteristics of this tumor. It is about a case report of pediatric patient admitted to a Pediatric Neonatal Reanimation, A. Harouchi Hospital, Ibn Rochd university Hospital centre, Casablanca. Results: We report the observation of a 4-day premature newborn who was hospitalized for exploration of an abdominal mass occupying the right flank since birth. Abdominal ultrasonography revealed a predominantly fleshy right solidocystic renal mass, a site of calcifications laminating the cortex, measuring 57x33x58, with minimal pyelocaliceal dilatation and diffuse infiltration of perrenal fat. The CT scan revealed a kidney increased in size, seat of a voluminous mass rather well limited, of tissue density, heterogeneous, seat of necrosis, realizing a sign of the spur, measuring 40x47x58mm. The diagnosis was confirmed by a kidney biopsy. Conclusion: Mesoblastic nephroma is considered a benign tumor. The diagnosis is discussed on the basis of clinical data, ultrasound and CT scan. Surgery is the primary treatment for NMC and is based on extended nephrectomy. Most patients with NMC have a favorable outcome, the overall prognosis is very good. VL - 9 IS - 1 ER -
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